Chronic granulomatous disease – primary phagocytic immunodeficiency
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Publication date: 2009-09-28
Cent Eur J Immunol 2009;34(3):182-191
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ABSTRACT
Chronic granulomatous disease (CGD) is a rare hereditary primary immunodeficiency, in which defective production of microbicidal oxidants by phagocytes (neutrophils, eosinophils, monocytes, and macrophages) leads to severe recurrent infections. This article reviews pathogenesis, diagnostic criteria, clinical signs, and treatment of CGD.